目次

O​verview including classification of sclerosing cholangitis.- Epidemiology.- Pathophysiology.- Pathology.- Clinical features.- Serology.- Diagnostic criteria.- Imaging.- 1) US and CT.- 2) MRI with MRCP.- 3) ERCP.- 4) EUS and IDUS.- Differential diagnosis from primarysclerosing cholangitis.- Differential diagnosis from cholangiocarcinoma.- Tissue acquisition for histologic diagnosis.- Other organ involvements including autoimmune pancreatitis.- Treatment.- 1) Steroids.- 2) Immunomodulatory drugs.- 3) Rituximab.- Prognosis.- IgG4-related sclerosing cholangitis in America.- IgG4-related sclerosing cholangitis in Europe.- IgG4-related disease.